Category D57
Non-Billable Category
FY2027 Dataset
D57: Sickle-cell disorders
Parent Chapter: Chapter 3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
Notice on Coding Specificity: Category D57 is a 3-character heading and cannot be reported directly on healthcare claims. You must assign one of the specific child codes listed below.
Specific Child Codes in Category D57
| Code | Official Descriptor | Status | Action |
|---|---|---|---|
| D57.00 | Hb-SS disease with crisis, unspecified | Billable Code | View Code |
| D57.01 | Hb-SS disease with acute chest syndrome | Billable Code | View Code |
| D57.02 | Hb-SS disease with splenic sequestration | Billable Code | View Code |
| D57.03 | Hb-SS disease with cerebral vascular involvement | Billable Code | View Code |
| D57.04 | Hb-SS disease with dactylitis | Billable Code | View Code |
| D57.09 | Hb-SS disease with crisis with other specified complication | Billable Code | View Code |
| D57.1 | Sickle-cell disease without crisis | Billable Code | View Code |
| D57.20 | Sickle-cell/Hb-C disease without crisis | Billable Code | View Code |
| D57.211 | Sickle-cell/Hb-C disease with acute chest syndrome | Billable Code | View Code |
| D57.212 | Sickle-cell/Hb-C disease with splenic sequestration | Billable Code | View Code |
| D57.213 | Sickle-cell/Hb-C disease with cerebral vascular involvement | Billable Code | View Code |
| D57.214 | Sickle-cell/Hb-C disease with dactylitis | Billable Code | View Code |
| D57.218 | Sickle-cell/Hb-C disease with crisis with oth complication | Billable Code | View Code |
| D57.219 | Sickle-cell/Hb-C disease with crisis, unspecified | Billable Code | View Code |
| D57.3 | Sickle-cell trait | Billable Code | View Code |
| D57.40 | Sickle-cell thalassemia without crisis | Billable Code | View Code |
| D57.411 | Sickle-cell thalassemia, unsp, with acute chest syndrome | Billable Code | View Code |
| D57.412 | Sickle-cell thalassemia, unsp, with splenic sequestration | Billable Code | View Code |
| D57.413 | Sickle-cell thalassemia, unsp, with cerebral vascular invl | Billable Code | View Code |
| D57.414 | Sickle-cell thalassemia, unspecified, with dactylitis | Billable Code | View Code |
| D57.418 | Sickle-cell thalassemia, unsp, with crisis with oth comp | Billable Code | View Code |
| D57.419 | Sickle-cell thalassemia, unspecified, with crisis | Billable Code | View Code |
| D57.42 | Sickle-cell thalassemia beta zero without crisis | Billable Code | View Code |
| D57.431 | Sickle-cell thalassemia beta zero with acute chest syndrome | Billable Code | View Code |
| D57.432 | Sickle-cell thalassemia beta zero with splenic sequestration | Billable Code | View Code |
| D57.433 | Sickle-cell thalassemia beta zero with cereb vascular invl | Billable Code | View Code |
| D57.434 | Sickle-cell thalassemia beta zero with dactylitis | Billable Code | View Code |
| D57.438 | Sickle-cell thalassemia beta zero with crisis with oth comp | Billable Code | View Code |
| D57.439 | Sickle-cell thalassemia beta zero with crisis, unspecified | Billable Code | View Code |
| D57.44 | Sickle-cell thalassemia beta plus without crisis | Billable Code | View Code |
| D57.451 | Sickle-cell thalassemia beta plus with acute chest syndrome | Billable Code | View Code |
| D57.452 | Sickle-cell thalassemia beta plus with splenic sequestration | Billable Code | View Code |
| D57.453 | Sickle-cell thalassemia beta plus with cereb vascular invl | Billable Code | View Code |
| D57.454 | Sickle-cell thalassemia beta plus with dactylitis | Billable Code | View Code |
| D57.458 | Sickle-cell thalassemia beta plus with crisis with oth comp | Billable Code | View Code |
| D57.459 | Sickle-cell thalassemia beta plus with crisis, unspecified | Billable Code | View Code |
| D57.80 | Other sickle-cell disorders without crisis | Billable Code | View Code |
| D57.811 | Other sickle-cell disorders with acute chest syndrome | Billable Code | View Code |
| D57.812 | Other sickle-cell disorders with splenic sequestration | Billable Code | View Code |
| D57.813 | Other sickle-cell disorders with cerebral vascular invl | Billable Code | View Code |
| D57.814 | Other sickle-cell disorders with dactylitis | Billable Code | View Code |
| D57.818 | Other sickle-cell disorders with crisis with oth comp | Billable Code | View Code |
| D57.819 | Other sickle-cell disorders with crisis, unspecified | Billable Code | View Code |
| D57 | Sickle-cell disorders | Non-Billable | View Code |
| D57.0 | Hb-SS disease with crisis | Non-Billable | View Code |
| D57.2 | Sickle-cell/Hb-C disease | Non-Billable | View Code |
| D57.21 | Sickle-cell/Hb-C disease with crisis | Non-Billable | View Code |
| D57.4 | Sickle-cell thalassemia | Non-Billable | View Code |
| D57.41 | Sickle-cell thalassemia, unspecified, with crisis | Non-Billable | View Code |
| D57.43 | Sickle-cell thalassemia beta zero with crisis | Non-Billable | View Code |
| D57.45 | Sickle-cell thalassemia beta plus with crisis | Non-Billable | View Code |
| D57.8 | Other sickle-cell disorders | Non-Billable | View Code |
| D57.81 | Other sickle-cell disorders with crisis | Non-Billable | View Code |